Incontinentia pigmenti - side

Incontinentia pigmenti causes swirling pigmentation of the skin. It is seen more frequently in females. The skin lesions are divided into three stages. Blistering (with vesicles and bullae) present at birth or within 6 to 7 weeks, a verrucous (rough wart-like stage), and the final stage shows whorled and bizarre patterns of dark pigmentation (hyperpigmentation).